REMEDY : BNSSG referral pathways & Joint Formulary


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BNSSG Paediatric Joint Formulary

3.3 Conditions affecting sputum viscosity

Last edited: 15-08-2024

3.3.1 Cystic fibrosis

First line drugs Second line drugs Specialist drugs Secondary care drugs

 

Dornase alfa (TLS Red)

Ivacaftor (TLS Red)

Elexacaftor / Tezacaftor / Ivacaftor (TLS Red)

Tezacaftor / Ivacaftor (TLS Red)

Lumacaftor / Ivacaftor (TLS Red)

Hypertonic Sodium chloride 6% (Mucoclear®) or 7% (Nebusal®) (TLS Amber)

  • To be started on Specialist respiratory advice only